Pulmonary Langerhans cell histiocytosis concurrent with bronchial hyperresponsiveness on a nonsmoker adult presenting with spontaneous pneumothorax
نویسندگان
چکیده
منابع مشابه
Spontaneous pneumothorax in a case of pulmonary langerhans cell histiocytosis.
Langerhans Cell Histiocytosis (LCH) is a rare disease involving clonal proliferation of Langerhans cells, abnormal cells deriving from bone marrow and capable of migrating from skin to lymph nodes. Clinically, its manifestations range from isolated bone lesions to multisystem disease. The authors present the case of 37 years old male, first diagnosed with Pulmonary LCH (PLCH) 9 years before cur...
متن کاملpulmonary langerhans cell histiocytosis presenting as simultaneous bilateral spontaneous pneumothorax in a non-smoker patient
pulmonary langerhans cell histiocytosis (plch) is a rare idiopathic disorder that primarily affects young adult cigarette smokers. affected patients often present with cough and dyspnea and about 20% of patients present with or later develop pneumothorax. it is striking that more than 90% of patients are smokers. we report a very unusual case of plch in a 20-year- old male patient with no smoki...
متن کاملPulmonary Langerhans' cell histiocytosis presented with recurrent pneumothorax.
Pulmonary Langerhans' cell histiocytosis is a relatively unusual, interstitial lung disease. Several organ systems may be involved, including the lung, bone, liver, lymph nodes and brain. It is known to occur preferentially in heavy smokers, and the cases such as ours presenting pneumothorax as the major clinical manifestation are rare.
متن کامل[Adult pulmonary Langerhans cell histiocytosis].
Adult pulmonary Langerhans’ cell histiocytosis is a rare disorder of unknown aetiology that occurs predominantly in young smokers, with an incidence peak at 20–40 yrs of age. In adults, pulmonary involvement with Langerhans’ cell histiocytosis usually occurs as a single-system disease and is characterised by focal Langerhans’ cell granulomas infiltrating and destroying distal bronchioles. High-...
متن کامل[Adult pulmonary Langerhans' cell histiocytosis].
INTRODUCTION Adult pulmonary Langerhans'cell histiocytosis, also referred to as histiocytosis X, is a disorder of unknown etiology which affects preferentially young smokers. The disease is characterized by granulomatous lesions which progressively invade and destroy distal airways, leading to the formation of characteristic cicatricial kystic lesions. Florid granulomas contain numerous Langerh...
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ژورنال
عنوان ژورنال: Respiratory Medicine CME
سال: 2008
ISSN: 1755-0017
DOI: 10.1016/j.rmedc.2007.10.006